Antenatally Diagnosed Suprarenal Mature Cystic Teratoma with Down Syndrome

  • Aditya Pratap Singh Department of Pediatric Surgery, SMS Medical College Jaipur, Rajasthan, India.
  • Ramesh Tanger Department of Pediatric Surgery, SMS Medical College Jaipur, Rajasthan, India.
  • Maryem Ansari Department of Pathology, SMS Medical College Jaipur, Rajasthan, India.
  • Arun Kumar Gupta Department of Pediatric Surgery, SMS Medical College Jaipur, Rajasthan, India.
  • Dinesh Kumar Barolia Department of Pediatric Surgery, SMS Medical College Jaipur, Rajasthan, India.
Keywords: Mature cystic teratoma, Antenatal diagnosis, Suprarenal teratoma;, Down syndrome

Abstract

Background: Teratoma is a germ cell tumor (GCT) arising from totipotent stem cells that differentiate into the tissues that are foreign to the anatomic site. Teratoma at the suprarenal location is extremely rare. The associa-tion with the Down syndrome also makes it unusual.

Case Report: We are presenting here a case of one-year-old female infant with Down syndrome who had an antenatal diagnosis of right suprarenal mass. Laparotomy revealed a large cystic mass in the right suprarenal location which was completely excised. Right adrenal gland could not be seen separately from the mass. The histological diagnosis was a mature cystic teratoma.

Conclusion: Adrenal teratoma is rare and may be considered in the differential diagnosis of antenatally diag-nosed suprarenal lesion. Its association with Down syndrome is rare finding.

Author Biography

Aditya Pratap Singh, Department of Pediatric Surgery, SMS Medical College Jaipur, Rajasthan, India.

Assistant Professor, Department of Pediatric Surgery, SMS Medical College Jaipur, Rajasthan, India.

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Teratoma
Published
2018-09-23
How to Cite
1.
Singh A, Tanger R, Ansari M, Gupta A, Barolia D. Antenatally Diagnosed Suprarenal Mature Cystic Teratoma with Down Syndrome. ajcr [Internet]. 23Sep.2018 [cited 17Nov.2018];9(3):15. Available from: http://www.apspjcaserep.com/ojs1/index.php/ajcr/article/view/44